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中华医学超声杂志(电子版) ›› 2023, Vol. 20 ›› Issue (05) : 568 -571. doi: 10.3877/cma.j.issn.1672-6448.2023.05.019

病例报告

超声联合磁共振与病理对照诊断胎儿期阴道斜隔综合征一例
包艳娟, 杨小红(), 万亚平, 陈欣林, 赵胜, 张晓燕   
  1. 430070 武汉,湖北省妇幼保健院超声诊断科
    430070 武汉,湖北省妇幼保健院医学影像科
  • 收稿日期:2022-03-31 出版日期:2023-05-01
  • 通信作者: 杨小红
  • 基金资助:
    湖北省卫生厅科研基金(WJ2021M188)

A rare case of fetal obstructed hemivagina and ipsilateral renal agenesis diagnosed by ultrasound combined with magnetic resonance imaging

Yanjuan Bao, Xiaohong Yang(), Yaping Wan   

  • Received:2022-03-31 Published:2023-05-01
  • Corresponding author: Xiaohong Yang
引用本文:

包艳娟, 杨小红, 万亚平, 陈欣林, 赵胜, 张晓燕. 超声联合磁共振与病理对照诊断胎儿期阴道斜隔综合征一例[J]. 中华医学超声杂志(电子版), 2023, 20(05): 568-571.

Yanjuan Bao, Xiaohong Yang, Yaping Wan. A rare case of fetal obstructed hemivagina and ipsilateral renal agenesis diagnosed by ultrasound combined with magnetic resonance imaging[J]. Chinese Journal of Medical Ultrasound (Electronic Edition), 2023, 20(05): 568-571.

图1 妊娠30+3周胎儿影像学图像。图a:超声显示左肾轻度积水(黄色箭头),右肾未显示。图b:超声显示直肠前方、膀胱(红色短箭头)后方13 mm×10 mm大小的无回声区(红色箭头),其上方见一突起的管状无回声(蓝色箭头)。图c:磁共振T2加权成像冠状位显示左肾体积增大(黄色箭头)、左侧输尿管扩张(绿色短箭头)。右肾区未见明显肾脏显影,盆腔偏右侧见多个不规则囊性灶。图d:磁共振T2加权成像纵断位显示右下腹见多个不规则囊性灶(紫色箭头示囊性发育不良右肾可能,红色箭头示阴道积液可能)
图2 妊娠31+1周胎儿引产后病理。图a:泌尿生殖体统大体标本:红色箭头示左、右侧卵巢及附件;黄色短箭头示左、右侧子宫;绿色箭头示左侧输尿管,中上段扩张、末端狭窄,正常开口于膀胱;紫色箭头示右肾囊性发育不良、输尿管短小、异位开口。黑色短箭头示膀胱。图b:剪开右侧阴道斜隔,可见右侧输尿管异位开口于隔后腔(蓝色短箭头)。从右侧囊性发育不良的肾脏注入盐水,可见液体自异位开口处流出。图c:剪开左侧阴道,左侧宫颈可见发育良好的皱襞(蓝色箭头示),阴道斜隔呈无孔型(黑色箭头)。图d:剪开左侧宫腔,可见发育良好的宫体、宫腔(黄色箭头)及宫颈皱襞(蓝色箭头)。图e:剪开右侧阴道,可见发育不良的宫颈(蓝色箭头),未见宫颈皱襞且呈闭锁状。图f:剪开右侧宫腔,显示宫体发育不良,宫腔窄小(黄色箭头)
表1 阴道斜隔综合征系统分类
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