Imaging analysis of ultrasound in the diagnosis of Prune belly syndrome during the early second-trimester

doi:10.3877/cma.j.issn.1672-6448.2017.11.010

Abstract

Abstract:

Objective

To investigate the sonographic characteristics of prune belly syndrome (PBS) in early period of second trimester.

Methods

A total of 16 pregnancies with diagnosis of PBS were enrolled between January 2014 and March 2017. Their sonographic characteristics and autopsy outcomes were analyzed.

Results

Overdistension of fetal bladder and flimsy fetal abdominal wall were found in all 16 cases. And there were 5 cases found prenatally to be associated with other abnormalities, including single umbilical artery (2 cases), sacrococcygeal teratoma (1 case), spina bifida manifesta (1 case) and strephenopodia (1 case). All women decided to terminatethe pregnancy, and deficiency of the abdominal musculature and increased collagen fiber were found by autopsy. Because of the confusion of the huge bladder, one case associated with imperforate anus was missed by prenatal ultrasonography.

Conclusion

Prenatal diagnosis of PBS in early period of second trimester is very important, because the amniotic fluid volume is still enough to evaluate the fetal structure.

Key words: Ultrasound diagnosis, Early second-trimester, Prune-belly syndrome

Wei Shen, Ailu Cai, Zeyu Yang, Bing Wang, Xiaoguang Wang, Ting Li. Imaging analysis of ultrasound in the diagnosis of Prune belly syndrome during the early second-trimester[J]. Chinese Journal of Medical Ultrasound (Electronic Edition), 2017, 14(11): 846-850.

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URL: https://chaosheng.cma-cmc.com.cn/EN/10.3877/cma.j.issn.1672-6448.2017.11.010

https://chaosheng.cma-cmc.com.cn/EN/Y2017/V14/I11/846

Figures/Tables 3

References 17

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胎儿孕周	例数	膀胱大小	产前超声诊断	引产胎儿标本病理检查结果
13周	1	2.8 cm×1.7 cm×2.2 cm	PBS合并骶尾部包块	PBS合并骶尾部畸胎瘤
13^＋4周	1	4.2 cm×2.1 cm×2.4 cm	PBS合并单脐动脉	PBS合并单脐动脉，肛门闭锁
13^＋5周	1	3.5 cm×2.5 cm×3.1 cm	PBS合并单脐动脉、脐带短	PBS合并单脐动脉、脐带短
14^＋2周	1	5.3 cm×3.6 cm×5.2 cm	PBS合并脊柱裂	PBS合并脊柱裂
17^＋1周	1	8.2 cm×5.7 cm×6.8 cm	PBS合并足内翻	PBS合并足内翻

胎儿孕周	例数	膀胱大小	产前超声诊断	引产胎儿标本病理检查结果
13周	1	2.8 cm×1.7 cm×2.2 cm	PBS合并骶尾部包块	PBS合并骶尾部畸胎瘤
13^＋4周	1	4.2 cm×2.1 cm×2.4 cm	PBS合并单脐动脉	PBS合并单脐动脉，肛门闭锁
13^＋5周	1	3.5 cm×2.5 cm×3.1 cm	PBS合并单脐动脉、脐带短	PBS合并单脐动脉、脐带短
14^＋2周	1	5.3 cm×3.6 cm×5.2 cm	PBS合并脊柱裂	PBS合并脊柱裂
17^＋1周	1	8.2 cm×5.7 cm×6.8 cm	PBS合并足内翻	PBS合并足内翻

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