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中华医学超声杂志(电子版) ›› 2019, Vol. 16 ›› Issue (07) : 555 -559. doi: 10.3877/cma.j.issn.1672-6448.2019.07.011

所属专题: 妇产科超声影像学 产前超声 文献 妇产科超声

综述

先天性胆管扩张症与Caroli病
廖伊梅1, 文华轩1, 李胜利1,()   
  1. 1. 518028 南方医科大学附属深圳市妇幼保健院超声科
  • 收稿日期:2019-05-17 出版日期:2019-07-01
  • 通信作者: 李胜利

Congenital bile duct dilatation and Caroli′s disease

Yimei Liao1, Huaxuan Wen1, Shengli Li1()   

  • Received:2019-05-17 Published:2019-07-01
  • Corresponding author: Shengli Li
引用本文:

廖伊梅, 文华轩, 李胜利. 先天性胆管扩张症与Caroli病[J]. 中华医学超声杂志(电子版), 2019, 16(07): 555-559.

Yimei Liao, Huaxuan Wen, Shengli Li. Congenital bile duct dilatation and Caroli′s disease[J]. Chinese Journal of Medical Ultrasound (Electronic Edition), 2019, 16(07): 555-559.

图1 先天性胆管扩张分型示意图[2]
图2 胎儿先天性胆管扩张产前超声声像图[2]。孕妇,31岁,孕39周,患乙肝4年。患儿在2岁时手术治疗痊愈。图a为上腹部横切面显示腹中线偏右侧一CYST,呈圆形,囊内透声好,该包块位于GB的后方,实时超声下,稍侧动探头时该包块与胆囊相通;图b,c为门静脉长轴切面二维及彩色多普勒显示门静脉位于囊性包块的左后方,因受压而走行弯曲;图d为出生后第2天采用14 MHz高频探头检查,胆囊长轴切面显示胆囊位于囊性包块的前上方,包块与胆囊交通
图3 先天性胆管扩张合并胎儿宫内生长发育迟缓[2]。孕妇,30岁,孕2产1孕24周。图a为上腹部横切面显示腹中线偏右侧一CYST,囊内透声好,该包块位于GB的后下方,实时超声下,稍侧动探头时该包块与胆囊相通;图b为引产胎儿标本解剖腹侧观,清楚地显示胆总管的十二指肠上段及十二指肠后段呈CYST,而胰腺段的胆总管内径正常
图5 MRI图像显示"中央圆点征"[19](箭头所示)
图7 胎儿MRI显示肝内多发细小囊性病变,未显示中央圆点征[17](箭头所示)
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